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KMID : 1144020170130010037
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Journal of Korean Association for Disability and Oral Health
2017 Volume.13 No. 1 p.37 ~ p.42
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DENTAL TREATMENT FOR A PATIENT WITH NOONAN SYNDROME UNDER GENERAL ANESTHESIA - CASE REPORT -
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Seo Mee-Kyung
Song Ji-Soo
Shin Teo-Jeon
Hyun Hong-Keun
Kim Jung-Wook
Jang Ki-Taeg
Lee Sang-Hoon
Kim Young-Jae
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Abstract
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Noonan syndrome is a relatively common genetic disorder which is autosomal dominant. Prevalence of Noonan syndrome is varying from 0.04% to 0.1%. It is characterized by distinctive facial features, chest deformity, short stature and congenital heart disease. Oral findings in patient with Noonan syndrome include high arched palate, dental malocclusion, articulation difficulties, and micrognathia. The purpose of this case report is to describe dental treatment of a children with Noonan syndrome.
5 year old boy with Noonan syndrome visited to the Seoul National University Dental Hospital for dental treatment. Due to need for close monitoring, concern about seizure and poor cooperation, we planned to perform the dental treatment under general anesthesia. Under general anesthesia, caries treatment was successfully performed and there was no postoperative complications related to general anesthesia. High arched palate was observed which is characteristic in Noonan syndrome.
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KEYWORD
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Noonan syndrome, Dental treatment, General anesthesia, Oral manifestation
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